Neurological, otolaryngological and ophthalmological implications of Susac syndrome – a case report
B. Grygiel-Górniak, M. Puszczewicz, E. Czaplicka Department of Rheumatology and Internal Medicine, Poznan University of Medical Sciences, Poznan, Poland. bgrygiel@ump.edu.pl
Susac syndrome is an endotheliopathy affecting the arterioles of the brain, retina, and inner ear. Many cases of Susac syndrome are underdiagnosed, mainly at the early stages of the disease, while prompt diagnosis enables a speedy recovery. Immediate treatment can halt disease progression and even prevent future disability.
We report a case of Susac syndrome, describe the difficulties in the diagnosis of this case, and include a detailed history of a 35-year-old man via the presentation of extensive laboratory work-up and imaging studies. Audiometry showed sensorineural hearing loss of about 75 dB in the left ear. Ovoid lesions of the corpus callosum in magnetic resonance (MR) were present as were advanced binocular ophthalmological changes in fluorescent angiography. Methylprednisolone with acetylsalicylic acid and intravenous immunoglobulin (IVIG) were implemented with a positive outcome (clinical and audiometric improvement).
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To cite this article
B. Grygiel-Górniak, M. Puszczewicz, E. Czaplicka
Neurological, otolaryngological and ophthalmological implications of Susac syndrome – a case report
Eur Rev Med Pharmacol Sci
Year: 2016
Vol. 20 - N. 14
Pages: 3073-3077